Curriculum
Module 03 · 75 min

Protein Structure, Folding & Quality Control

From Anfinsen's dogma to chaperones, the UPS, and the unfolded-protein response.

CoreClinicalResearch
Topics

What this module covers

  • 01Levels of structure; Ramachandran constraints; intrinsically disordered proteins
  • 02Folding landscapes, kinetic traps, and chaperone-assisted folding (Hsp70, Hsp90, TRiC, GroEL)
  • 03Co-translational folding and ribosome-associated chaperones
  • 04Ubiquitin-proteasome system: E1/E2/E3, polyubiquitin chain types
  • 05Autophagy: macro-, micro-, chaperone-mediated; LC3 lipidation
  • 06ER unfolded-protein response: PERK, IRE1, ATF6 arms
  • 07Targeted protein degradation: PROTACs, molecular glues
Deep dives

Lesson sub-pages

Learning objectives

By the end of this module you will be able to

  • L01Predict, given a misfolding mutation, which quality-control branch will engage and which clinical phenotype is plausible.
  • L02Distinguish K48 from K63 polyubiquitin chains in cellular function.
  • L03Explain how a PROTAC differs mechanistically from a competitive inhibitor.
Expected takeaways

What you should walk away believing

  • Most cellular proteins fold with chaperone help — Anfinsen's dogma is a special case, not the rule.
  • Proteostasis collapse is a unifying mechanism in neurodegeneration, ageing, and many cancers.
  • Drugging the degradation machinery (PROTACs, molecular glues) opens previously 'undruggable' targets.
Core summary

At the Core level

Proteins fold along energy landscapes shaped by their amino-acid sequence; the cell helps with chaperones, monitors with quality control, and disposes of failures with the proteasome or autophagy. When proteostasis fails — by mutation, age, or stress — proteins aggregate. Aggregation is not a passive end state; it is a signal that triggers stress responses, inflammation, and ultimately cell death.

Myth vs reality

Common misconception

Claim

AlphaFold has 'solved' protein structure.

Reality

AlphaFold predicts a single low-energy state of a single chain remarkably well. Conformational dynamics, complex assemblies, post-translational modifications, and disordered regions remain hard.

Evidence-graded claims

Claims, scored A–F

A
Proteasome inhibitors are first-line in multiple myeloma
Standard of care worldwide.
C
AlphaFold structures can be used directly for drug design
Useful for orientation; binding-pocket geometry often needs experimental refinement.
E
Heat-shock-protein induction extends human healthspan
Strong in worms/flies; unproven and oversold in humans.
Quiz

Check your understanding

Q1. Which polyubiquitin linkage canonically targets proteins for proteasomal degradation?
Q2. PROTACs work by:
Flashcards

Lock it in

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Three arms of the ER UPR?
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Suggested reading

Primary literature